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Case Report

Exp Neurobiol 2015; 24(3): 252-255

Published online September 30, 2015

© The Korean Society for Brain and Neural Sciences

Neuro-Behçet’s Disease Presenting as Hypertrophic Pachymeningitis

Byung-Nam Yoon1, Soo-Jung Kim1, Mi-Jin Lim2, Jee-Young Han3, Kwang-Woo Lee3, Jung-Joon Sung3, Choong Kun Ha1 and Seong Hye Choi1*

1Department of Neurology, 2Division of Rheumatology, Department of Internal Medicine, Inha University Hospital, Incheon 22332, 3Department of Neurology, Seoul National University Hospital, College of Medicine, Seoul 03080, Korea

Correspondence to: *To whom correspondence should be addressed.
TEL: 82-32-890-3668, FAX: 82-32-890-3097

Received: June 2, 2015; Revised: August 22, 2015; Accepted: September 8, 2015


A 25-year-old man presented with blurred vision and chronic headache. His brain MRI revealed bilateral frontal pachymeningeal enhancement with leptomeningeal enhancement. The patient had experienced recurrent oral ulcer and had anterior uveitis and papulopustules skin lesion. We diagnosed him with hypertrophic pachymeningitis (HP) associated with neuro-Behçet's disease (NBD). There have been few reports describing HP in patients with NBD. We report a case of NBD presenting as HP.

Keywords: Behç,et’s disease, neuro-Behç,et’s disease, Hypertrophic pachymeningitis